A novel case of congenital hepatic arterio-veno-portal shunts with umbilical vein aneurysm

A novel case of congenital hepatic arterio-veno-portal shunts with umbilical vein aneurysm

Blog Article

A term male infant presented with Railing Hardware congenital hepatic arterio-veno-portal shunts.A mass-like lesion in the left lobe of the liver received blood supply from not only the umbilical vein, but also the hepatic and inferior intrahepatic arteries, communicating with the hepatic and portal veins in a complicated manner, with an umbilical vein aneurysm.The blood flow of the arterio-veno-portal shunts spontaneously and gradually declined from the Walkie Talkies neonatal period to six years of age.Although mild high-output cardiac failure had developed, no life-threatening events or health problems originating from portosystemic shunts, such as pulmonary artery hypertension and hepatopulmonary syndrome, were observed.However, this report shows that scrupulous follow-up to identify pulmonary artery hypertension and hepatopulmonary syndrome should be continued because complete resolution of the arterio-veno-portal shunts was not obtained in this case.